Uhl's anomaly: Absence of the right ventricular myocardium.
作者信息
Ganczar Joanna, English Robert
机构信息
Department of Pediatrics, College of Medicine, University of Florida, Jacksonville, Florida, USA.
Department of Pediatric Cardiology, College of Medicine, University of Florida, Jacksonville, Florida, USA.
出版信息
Ann Pediatr Cardiol. 2015 Jan-Apr;8(1):71-3. doi: 10.4103/0974-2069.149529.
Abstract
We report a case of Uhl's anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.
摘要
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