Mohanty Vivek, Sharma Shubham Kumar, Goswami Sourabh, Gudhage Rahul, Deora Surender
Department of Cardiology, All India Institute of Medical Sciences, Jodhpur, Rajasthan, India.
Avicenna J Med. 2023 Mar 24;13(1):56-59. doi: 10.1055/s-0043-1764376. eCollection 2023 Jan.
Idiopathic isolated right ventricular cardiomyopathy is an extremely rare cause of right ventricular failure. Here, we report a case of 65-year-old male presented with chief complaints of dyspnea, fatigue, and bilateral pedal edema for the last 6 months. On clinical evaluation, grade II/III pansystolic murmur was present in left parasternal area. Investigations and imaging revealed dilated right atrium and ventricle with normal pulmonary artery pressure without any etiology. Magnetic resonance imaging ruled out other common causes of right ventricular cardiomyopathy; thus, the patient was diagnosed as a case of idiopathic isolated right ventricular cardiomyopathy that is a diagnosis of exclusion.
特发性孤立性右心室心肌病是导致右心室衰竭的极其罕见的病因。在此，我们报告一例65岁男性患者，在过去6个月中主要表现为呼吸困难、乏力和双侧足背水肿。临床评估发现，左胸骨旁区存在II/III级全收缩期杂音。检查和影像学检查显示右心房和右心室扩张，肺动脉压正常，且无任何病因。磁共振成像排除了右心室心肌病的其他常见病因；因此，该患者被诊断为特发性孤立性右心室心肌病，此诊断为排除性诊断。
