Kumar Vinod, Nair Rajesh, Upadhyaya Sunil, Nayal Bhavna, Shetty Arjun
Assistant Professor, Department of Neurosurgery, Kasturba Hospital , Manipal, India .
Registrar, Kasturba Hospital , India .
J Clin Diagn Res. 2015 Jan;9(1):XD09-XD10. doi: 10.7860/JCDR/2015/10644.5498. Epub 2015 Jan 1.
Adenoid cystic carcinoma (ACC) is a rare malignant tumour of the major salivary glands. It accounts for 10-15% of all salivary gland tumours and 1% of all head and neck tumours. Surgical resection followed by radiation is the choice of treatment for ACC. However, late loco-regional recurrence and metastasis is often seen emphasizing the importance of long-term follow-up. We report an unusual case of extradural metastasis of ACC in the dorsal spine. The primary submandibular gland tumour was resected 11 y back. A recurrence had been detected two years prior to the occurrence of spinal metastasis. Surgical decompression was done which was followed by palliative radiotherapy. Patient is symptomatically better, ambulant and on regular follow-up.
腺样囊性癌（ACC）是一种发生于大唾液腺的罕见恶性肿瘤。它占所有唾液腺肿瘤的10% - 15%，占所有头颈部肿瘤的1%。手术切除后辅以放疗是腺样囊性癌的治疗选择。然而，局部区域晚期复发和转移较为常见，这凸显了长期随访的重要性。我们报告了一例发生于脊柱背侧的腺样囊性癌硬膜外转移的罕见病例。原发性下颌下腺肿瘤于11年前切除。在脊柱转移发生前两年检测到复发。进行了手术减压，随后进行了姑息性放疗。患者症状有所改善，能够行走并接受定期随访。
