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临床未怀疑的特发性CD4淋巴细胞减少症中的孤立性皮肤隐球菌病。

Isolated cutaneous cryptococcosis in clinically unsuspected idiopathic CD4 lymphocytopenia.

作者信息

Sharma Divya, Singh Neha, Kaushal Seema, Jain Shyama

机构信息

Department of Pathology, Maulana Azad Medical College and Associated LNJP Hospital, New Delhi, India.

出版信息

J Cytol. 2014 Oct-Dec;31(4):230-2. doi: 10.4103/0970-9371.151143.

DOI:10.4103/0970-9371.151143
PMID:25745296
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4349021/
Abstract

Idiopathic CD4 lymphocytopenia first defined in 1992 by the U.S. Centers for Disease Control and Prevention, as the repeated presence of a CD4(+) T-lymphocyte count of fewer than 300 cells/cumm or of <20% of total T-cells with no evidence of human immunodeficiency virus (HIV) infection and therapy that might cause depressed CD4 T-cells. Most of the cases present with systemic opportunistic infections. We report a case without risk factors or laboratory evidence of HIV infection, presenting with cutaneous cryptococcal infection, diagnosed on cytology.

摘要

特发性CD4淋巴细胞减少症于1992年由美国疾病控制与预防中心首次定义,即CD4(+) T淋巴细胞计数反复低于300个细胞/立方毫米或占总T细胞的比例不足20%,且无人类免疫缺陷病毒(HIV)感染及可能导致CD4 T细胞减少的治疗证据。大多数病例会出现全身性机会性感染。我们报告一例无HIV感染风险因素或实验室证据的病例,该病例表现为皮肤隐球菌感染,经细胞学检查确诊。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fff2/4349021/43d2c0001be3/JCytol-31-230-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fff2/4349021/9c5da6c09b69/JCytol-31-230-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fff2/4349021/43d2c0001be3/JCytol-31-230-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fff2/4349021/9c5da6c09b69/JCytol-31-230-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fff2/4349021/43d2c0001be3/JCytol-31-230-g002.jpg

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本文引用的文献

1
Idiopathic CD4+ lymphocytopenia in Hispanic male: case report and literature review.西班牙裔男性特发性CD4 +淋巴细胞减少症:病例报告及文献综述
Int Med Case Rep J. 2014 Jul 30;7:117-20. doi: 10.2147/IMCRJ.S63836. eCollection 2014.
2
Idiopathic CD4 lymphocytopenia: clinical and immunologic characteristics and follow-up of 40 patients.特发性CD4淋巴细胞减少症:40例患者的临床和免疫学特征及随访
Medicine (Baltimore). 2014 Mar;93(2):61-72. doi: 10.1097/MD.0000000000000017.
3
Idiopathic CD4 Lymphocytopenia: Spectrum of opportunistic infections, malignancies, and autoimmune diseases.
特发性CD4淋巴细胞减少症:机会性感染、恶性肿瘤和自身免疫性疾病谱
Avicenna J Med. 2013 Apr;3(2):37-47. doi: 10.4103/2231-0770.114121.
4
Idiopathic CD4 lymphocytopenia presenting as refractory cryptococcal meningitis.以难治性隐球菌性脑膜炎为表现的特发性CD4淋巴细胞减少症。
Ann Indian Acad Neurol. 2010 Apr;13(2):136-8. doi: 10.4103/0972-2327.64646.
5
Idiopathic CD4+ lymphocytopenia: natural history and prognostic factors.特发性CD4+淋巴细胞减少症:自然病史及预后因素。
Blood. 2008 Jul 15;112(2):287-94. doi: 10.1182/blood-2007-12-127878. Epub 2008 May 2.
6
Idiopathic CD4+ lymphocytopenia may be due to decreased bone marrow clonogenic capability.特发性CD4+淋巴细胞减少症可能是由于骨髓克隆能力下降所致。
Int Arch Allergy Immunol. 2005 Apr;136(4):379-84. doi: 10.1159/000084258. Epub 2005 Mar 2.
7
Cutaneous cryptococcosis--primary versus secondary disease. Report of two cases with review of literature.
Am J Dermatopathol. 1993 Aug;15(4):372-7.
8
Idiopathic CD4+ T-lymphocytopenia.
N Engl J Med. 1993 Sep 30;329(14):1045-6. doi: 10.1056/NEJM199309303291418.
9
Unexplained opportunistic infections and CD4+ T-lymphocytopenia without HIV infection. An investigation of cases in the United States. The Centers for Disease Control Idiopathic CD4+ T-lymphocytopenia Task Force.无HIV感染情况下的不明原因机会性感染和CD4 + T淋巴细胞减少症。美国病例调查。疾病控制中心特发性CD4 + T淋巴细胞减少症工作组。
N Engl J Med. 1993 Feb 11;328(6):373-9. doi: 10.1056/NEJM199302113280601.
10
Unexplained CD4+ T-lymphocyte depletion in persons without evident HIV infection--United States.美国无明显人类免疫缺陷病毒(HIV)感染人群中原因不明的CD4 + T淋巴细胞耗竭
MMWR Morb Mortal Wkly Rep. 1992 Jul 31;41(30):541-5.