Department of Paediatric Urology, Royal Manchester Children's Hospital, Manchester M13 9WL, United Kingdom.
Department of Paediatric Radiology, Royal Manchester Children's Hospital, Manchester M13 9WL, United Kingdom.
J Pediatr Surg. 2020 Sep;55(9):e4-e5. doi: 10.1016/j.jpedsurg.2012.07.033. Epub 2015 Jan 8.
Isolated urogenital sinus can cause distended bladder and/or vagina and may present with an abdominal mass and sepsis during infancy. Older children may present with recurrent urinary tract infections and hematocolpos. We describe a 3-year-old girl with recurrent urinary tract infections thought to be secondary to vesicoureteric reflux. On further investigation, an isolated urogenital sinus anomaly with a calculus inside one of the hemivaginae was noted. She was managed expectantly with a plan to intervene at puberty. At puberty, during removal of the stone, the hemivaginal introitus was found to be stenotic. Gradually increasing sizes of Amplatz type graduated renal dilators were introduced from the introitus of the urogenital sinus into the hemivaginal stone until a size 22F Amplatz sheath could be passed easily. Size 10F cystoscope was passed through this channel, and the stone was fragmented using electrohydraulic lithotripsy. At a later date, she underwent staged anterior sagittal transvulval mobilization of the urogenital sinus.
孤立性尿生殖窦可导致膀胱和/或阴道扩张,并可在婴儿期出现腹部肿块和败血症。年龄较大的儿童可能会出现反复尿路感染和阴道积血。我们描述了一名 3 岁女孩,因反复尿路感染,被认为是膀胱输尿管反流引起的。进一步检查发现,存在孤立性尿生殖窦畸形,其中一个半阴道内有结石。她接受了期待治疗,计划在青春期进行干预。青春期时,在取出结石的过程中,发现半阴道入口狭窄。从尿生殖窦的入口逐渐向半阴道结石中插入大小为 Amplatz 型的逐渐增大的肾扩张器,直到可以轻松插入 22F 的 Amplatz 护套。大小为 10F 的膀胱镜通过这个通道插入,并使用液电碎石术将结石打碎。在以后的日子里,她接受了分期经阴道前矢状位尿生殖窦移动术。