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睡眠起始时出现的腹部不安和类似脊髓固有肌阵挛:一种不寻常的重叠综合征。

A restless abdomen and propriospinal myoclonus like at sleep onset: an unusual overlap syndrome.

作者信息

Baiardi Simone, La Morgia Chiara, Mondini Susanna, Cirignotta Fabio

机构信息

Department of Biomedical and Neuromotor Sciences, University of Bologna, Neurology Unit, S. Orsola-Malpighi Hospital, AOU Bologna, Italy.

出版信息

BMJ Case Rep. 2015 Mar 27;2015:bcr2014206679. doi: 10.1136/bcr-2014-206679.

Abstract

We report for the first time the association between restless abdomen, a phenotypic variant of restless legs syndrome in which symptoms are limited to the abdomen, and propriospinal myoclonus at sleep onset causing severe insomnia. The treatment with a low-dosage of dopaminergic drug (pramipexole) induced the immediate disappearance of both symptoms, which was documented by video-polysomnography.

摘要

我们首次报告了不安腹部(不安腿综合征的一种表型变异,其症状仅限于腹部)与入睡时脊髓性肌阵挛导致严重失眠之间的关联。低剂量多巴胺能药物(普拉克索)治疗使两种症状立即消失,这通过视频多导睡眠图得到了证实。

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本文引用的文献

1
Propriospinal myoclonus: clinical reappraisal and review of literature.脊髓性肌阵挛:临床重新评估及文献综述
Neurology. 2014 Nov 11;83(20):1862-70. doi: 10.1212/WNL.0000000000000982. Epub 2014 Oct 10.
2
Psychogenic axial myoclonus: clinical features and long-term outcome.心因性轴索性肌阵挛:临床特征与长期预后
Parkinsonism Relat Disord. 2014 Jun;20(6):596-9. doi: 10.1016/j.parkreldis.2014.02.026. Epub 2014 Mar 13.
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Restless abdomen: a phenotypic variant of restless legs syndrome.不安腹部:不安腿综合征的一种表型变异。
Neurology. 2011 Sep 27;77(13):1283-6. doi: 10.1212/WNL.0b013e318230207a. Epub 2011 Sep 14.
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Propriospinal myoclonus at sleep onset.睡眠起始时的脊髓性肌阵挛
Neurophysiol Clin. 2006 Sep-Dec;36(5-6):351-5. doi: 10.1016/j.neucli.2006.12.004. Epub 2007 Jan 26.

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