Dhanger Sangeeta, Adinarayanan Sethuramachandran, Vinayagam Stalin, Kumar Mohanasundaram Praveen
Department of Anaesthesiology and Critical Care, Indira Gandhi Medical College and Research Institute, Puducherry, India.
Department of Anaesthesiology and Critical Care, Jawaharlal Institute of Postgraduate Medical Education and Research, Puducherry, India.
Saudi J Anaesth. 2015 Apr-Jun;9(2):217-9. doi: 10.4103/1658-354X.152893.
Morquio's syndrome, also known as mucopolysaccharidosis type IV is an autosomal recessive disorder, caused by deficiency of n-acetylgalactosamine-6-sulphate. Anesthetic management of this syndrome is a great challenge, especially in pediatric age group as "cannot ventilate, cannot intubate" scenario can be encountered by anesthesiologist due to the possibility of total airway collapse. Herewith, we are reporting a case of child with Morquio's syndrome where I-gel assisted fiber-optic intubation was used for safe endotracheal intubation.
莫尔基奥综合征,也称为IV型黏多糖贮积症,是一种常染色体隐性疾病,由N-乙酰半乳糖胺-6-硫酸盐缺乏引起。该综合征的麻醉管理极具挑战性,尤其是在儿科患者中,因为麻醉医生可能会遇到“无法通气、无法插管”的情况,这是由于气道可能完全塌陷。在此,我们报告一例患有莫尔基奥综合征的儿童病例,其中使用了I-gel喉罩辅助纤维支气管镜插管以安全地进行气管插管。