成人莫尔奎氏综合征的麻醉考虑因素 - 病例报告。
Anaesthetic considerations of adults with Morquio's syndrome - a case report.
机构信息
Department of Anaesthesia and Critical Care, Adelaide and Meath National Children Hospital Dublin, Dublin, Ireland.
出版信息
BMC Anesthesiol. 2010 Feb 26;10:2. doi: 10.1186/1471-2253-10-2.
BACKGROUND
The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx.
CASE PRESENTATION
Herein we describe the anaesthetic considerations and management of a 26 year old adult with Morquio syndrome, who presented for an elective hip replacement.
CONCLUSION
This report details an awake fiberoptic intubation in an adult with Morquio syndrome. We recommend that this approach be considered in patients with Morquio syndrome undergoing general anaesthesia.
背景
黏多糖贮积症患者的麻醉管理较为复杂，涉及多种因素，包括齿状突发育不全、寰枢椎不稳定、胸腰椎后凸畸形以及口咽部软组织黏多糖沉积。
病例报告
本文描述了 1 例 26 岁黏多糖贮积症成年患者的麻醉处理，该患者因择期髋关节置换入院。
结论
本报告详细介绍了 1 例黏多糖贮积症成年患者清醒纤维支气管镜插管的情况。我们建议在接受全身麻醉的黏多糖贮积症患者中考虑这种方法。
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