Al-Balushi Asim, Al-Kindi Hamood, Al-Shuaili Hamood, Kumar Suresh, Al-Maskari Salim
Department of Pediatric Cardiology, Royal Hospital, Muscat, Oman.
Department of Cardiothoracic Surgery, Sultan Qaboos University Hospital, Muscat, Oman.
Oman Med J. 2015 Jan;30(1):26-30. doi: 10.5001/omj.2015.05.
The aim of our study was to examine the spectrum, demographics, and mortality rate among adolescents and adults with congenital heart diseases (CHD) in Oman.
Data was collected retrospectively from the Royal Hospital, Muscat, electronic health records for all patients with a diagnosis of CHD aged 13 years and above. Data was analyzed according to the type of CHD and in-hospital mortality was assessed using Kaplan-Meier survival analysis.
A total of 600 patients with CHD were identified, among them 145 (24%) were aged 18 years or below. The median age was 24 years. The majority of patients had a simple form of CHD. Atrial and ventricular septal defects together constituted 62.8% of congenital heart diseases. Most patients were clustered in Muscat (32%) and the Batinah regions (31.1%) of Oman. Patients with tetralogy of Fallot and Fontan had shorter survival time than recorded in the published literature.
Mostly simple forms of CHD in younger patients was observed. The survival rate was significantly shortened in more complex lesions compared to simple lesions. A national data registry for CHD is needed to address the morbidities and mortality associated with the disease.
我们研究的目的是调查阿曼青少年及成人先天性心脏病（CHD）患者的疾病谱、人口统计学特征及死亡率。
回顾性收集马斯喀特皇家医院13岁及以上确诊为CHD的所有患者的电子健康记录数据。根据CHD类型进行数据分析，并采用Kaplan-Meier生存分析评估住院死亡率。
共识别出600例CHD患者，其中145例（24%）年龄在18岁及以下。中位年龄为24岁。大多数患者患有简单型CHD。房间隔缺损和室间隔缺损共占先天性心脏病的62.8%。大多数患者集中在阿曼的马斯喀特地区（32%）和巴提奈地区（31.1%）。法洛四联症和Fontan手术患者的生存时间比已发表文献中记录的更短。
观察到年轻患者中大多为简单型CHD。与简单病变相比，更复杂病变的生存率显著缩短。需要建立一个全国性的CHD数据登记系统，以应对与该疾病相关的发病率和死亡率问题。
