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肝动脉动脉瘤破裂:结节性多动脉炎的一种不寻常表现。

Ruptured hepatic artery aneurysm: an unusual presentation of polyarteritis nodosa.

作者信息

Wicherts D A, Bruntink M M, Demirkiran A, van Santvoort H C, van Lienden K P, Ambarus C A, Besselink M G H, van Gulik T M

机构信息

Department of Surgery, Academic Medical Center, Amsterdam, The Netherlands.

Department of Surgery, Red Cross Hospital, Beverwijk, The Netherlands.

出版信息

BMJ Case Rep. 2015 Apr 1;2015:bcr2014208240. doi: 10.1136/bcr-2014-208240.

Abstract

A 52-year-old woman presented with severe acute right upper quadrant abdominal pain and signs of intra-abdominal haemorrhage. CT and selective angiography revealed a ruptured right hepatic artery aneurysm and diffuse aneurysmatic disease involving most intra-abdominal organs, suggestive of polyarteritis nodosa. Although treatment with high-dose steroids was initiated, the patient died of progressive bowel ischaemia.

摘要

一名52岁女性因严重的急性右上腹腹痛及腹腔内出血迹象就诊。CT和选择性血管造影显示右肝动脉动脉瘤破裂,且弥漫性动脉瘤病累及多数腹腔内器官,提示结节性多动脉炎。尽管开始了大剂量类固醇治疗,但患者死于进行性肠缺血。

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