Doucet Katie M, Labinaz Marino, Chandy George, Mielniczuk Lisa, Stewart Duncan, Contreras-Dominguez Vladimir, Pugliese Carolyn, Dennie Carole, Burwash Ian G, Davies Ross A
Divisions of Cardiology and Nursing, University of Ottawa, Ottawa, Ontario, Canada.
Divisions of Respirology and Internal Medicine, University of Ottawa, Ottawa, Ontario, Canada.
Can J Cardiol. 2015 Apr;31(4):548.e5-7. doi: 10.1016/j.cjca.2014.12.025. Epub 2014 Dec 24.
We describe a patient with fibrosing mediastinitis after childhood histoplasmosis who presented with severe pulmonary hypertension secondary to pulmonary vein stenoses. Stenting of 2 stenosed pulmonary veins via a transseptal approach resulted in an immediate decrease in systolic pulmonary artery pressure from 90 to 68 mm Hg and improvement in dyspnea and cardiac index, which was sustained at 6 months. This case highlights the importance of routinely assessing the pulmonary veins during workup for pulmonary hypertension.
我们描述了一名儿童期组织胞浆菌病后发生纤维性纵隔炎的患者,该患者因肺静脉狭窄出现严重肺动脉高压。经房间隔途径对2条狭窄的肺静脉进行支架置入术,使收缩期肺动脉压立即从90 mmHg降至68 mmHg,并改善了呼吸困难和心脏指数,这种改善在6个月时仍持续存在。该病例强调了在肺动脉高压检查过程中常规评估肺静脉的重要性。