Kotarać Milutin, Radovanović Nebojša, Lekić Nebojša, Ražnatović Zoran, Djordjević Vladimir, Lekć Dragana, Sagić Dragan
Srp Arh Celok Lek. 2015 Jan-Feb;143(1-2):74-8. doi: 10.2298/sarh1502074k.
Median arcuate ligament (MAL) syndrome, also called celiac trunk compression syndrome (CACS) or Dunbar syndrome is a rare disorder caused by compression of the celiac artery by median arcuate ligament of the diaphragm, which leads to mesenteric ischemia and chronic abdominal angina. The typical clinical triad of symptoms includes postprandial epigastric pain, weight loss and vomiting. The gold standard for MAL syndrome diagnosis is selective angiography, while in symptomatic patients with angiographically verified stenosis the optimal therapy is surgical treatment.
A 40-year-old male patient was presented with epigastric pain, followed by dyspepsia and weight loss. The upper endoscopy showed gastric and duodenal distention with prominent folds of gastric mucosa and slow peristalsis. Selective angiography showed stenosis (90%) of initial segment of the celiac trunk. Adhesiolysis with the transection of the median arcuate ligament was performed. Due to repeated symptoms, the patient was reoperated on the 10th postoperative day with performed adhesiolysis and gastrostomy for gastric nutrition. Two months later, the patient was rehospitalized for closure of gastrostomy. At five years follow-up, selective angiography showed no stenosis of the initial segment of the celiac artery.
Despite the existing controversy concerning pathophysiological mechanism, the clinical presentation and treatment modalities of patients with MAL syndrome, it is evident that careful selection and adequate surgical treatment may significantly reduce symptoms in these patients.
正中弓状韧带综合征,也称为腹腔干压迫综合征(CACS)或邓巴综合征,是一种罕见的疾病,由膈肌正中弓状韧带压迫腹腔动脉导致肠系膜缺血和慢性腹部绞痛。典型的临床三联征症状包括餐后上腹部疼痛、体重减轻和呕吐。正中弓状韧带综合征诊断的金标准是选择性血管造影,而对于血管造影证实有狭窄的有症状患者,最佳治疗方法是手术治疗。
一名40岁男性患者出现上腹部疼痛,随后出现消化不良和体重减轻。上消化道内镜检查显示胃和十二指肠扩张,胃黏膜皱襞突出,蠕动缓慢。选择性血管造影显示腹腔干起始段狭窄(90%)。进行了正中弓状韧带切断粘连松解术。由于症状反复,患者在术后第10天再次手术,进行了粘连松解术并做了胃造口术以提供胃营养。两个月后,患者因胃造口术闭合再次住院。在五年的随访中,选择性血管造影显示腹腔动脉起始段无狭窄。
尽管关于正中弓状韧带综合征患者的病理生理机制、临床表现和治疗方式存在争议,但很明显,仔细选择和适当的手术治疗可以显著减轻这些患者的症状。