Yap Desmond Y H, Lai Kar N
Nephrology Division, Department of Medicine, The University of Hong Kong, Hong Kong, China.
Int J Mol Sci. 2015 Apr 9;16(4):7917-31. doi: 10.3390/ijms16047917.
Lupus nephritis (LN) is a common and severe organ manifestation of systemic lupus erythematosus (SLE), and is associated with significant patient morbidity and mortality. Autoantibodies and aberrations in lymphocyte subsets have putative roles in the pathogenesis of SLE and LN, and might reflect disease activity and are amenable to immunosuppressive treatments. Anti-DNA is one of the well-studied autoantibodies, which correlates with disease activity and has direct nephritogenic effects on resident renal cells and various glomerular components. Other important autoantibodies in the pathogenesis of LN include anti-C1q, anti-α-actinin and anti-nucleosome antibodies. Changes in naive and memory B cells and plasma cells have been observed in SLE and LN patients. These B cell subsets exert diverse effects during pathogenesis of LN such as production of autoantibodies, secretion of proinflammatory and anti-inflammatory cytokines and presentation of auto-antigens to effector cells. Aberration of T lymphocytes, especially the T-helper subsets, is also highly pertinent in the development of LN. In this context, important T helper subsets include Th1, Th2, Th9, Th17, TReg and follicular T-helper cells. The growing knowledge on these autoantibodies and lymphocyte subset abnormalities will enhance our understanding of SLE and LN, and hence help devise better strategies for disease monitoring and treatment.
狼疮性肾炎(LN)是系统性红斑狼疮(SLE)常见且严重的器官表现,与患者的高发病率和死亡率相关。自身抗体及淋巴细胞亚群异常在SLE和LN的发病机制中具有假定作用,可能反映疾病活动情况,且可通过免疫抑制治疗进行调节。抗DNA抗体是研究较为充分的自身抗体之一,它与疾病活动相关,对肾脏固有细胞和各种肾小球成分具有直接致肾炎作用。LN发病机制中的其他重要自身抗体包括抗C1q、抗α - 辅肌动蛋白和抗核小体抗体。在SLE和LN患者中已观察到初始B细胞、记忆B细胞和浆细胞的变化。这些B细胞亚群在LN发病过程中发挥多种作用,如产生自身抗体、分泌促炎和抗炎细胞因子以及将自身抗原呈递给效应细胞。T淋巴细胞异常,尤其是辅助性T细胞亚群异常,在LN的发生发展中也高度相关。在此背景下,重要的辅助性T细胞亚群包括Th1、Th2、Th9、Th17、调节性T细胞(TReg)和滤泡辅助性T细胞。对这些自身抗体和淋巴细胞亚群异常的认识不断增加,将增进我们对SLE和LN的理解,从而有助于制定更好的疾病监测和治疗策略。