Hood Hunter W, Dodge-Khatami Ali, Parnell Aimee S, Salazar Jorge D
Pediatric and Congenital Heart Surgery, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA.
Pediatric and Congenital Heart Surgery, Children's Heart Center, University of Mississippi Medical Center, Jackson, MS, USA
World J Pediatr Congenit Heart Surg. 2015 Apr;6(2):307-10. doi: 10.1177/2150135114561689.
A neonate with prenatally diagnosed large intracardiac rhabdomyomas and suspicion of tuberous sclerosis presented at birth with severe ductal-dependent obstruction at the tricuspid valve and an atrial septal defect (ASD). Biventricular repair at 9 days of life included tumor resection, repair of the posterior leaflet of the tricuspid valve with autologous pericardium, fenestrated ASD closure, and ductus ligation. After an uneventful postoperative recovery, follow-up echocardiography at two months showed excellent results with tricuspid valve competency and normal biventricular function. Overall prognosis will probably depend on issues pertaining to tuberous sclerosis.
