Wu Chuangyan, Wang Yixuan, Su Wei, Xia Jiahong, Dong Nianguo, Wang Guohua
Department of Cardiovascular Surgery, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, China.
J Card Surg. 2019 Oct;34(10):1123-1126. doi: 10.1111/jocs.14191. Epub 2019 Aug 2.
Primary cardiac tumors are very rare and generally benign. The most common type, cardiac rhabdomyoma, comprises 45% to 75% of primary cardiac tumors. Cardiac rhabdomyoma is a rare benign tumor that commonly presents with tuberous sclerosis. We present a case of an infant with multifocal cardiac rhabdomyomas with an atrial septal defect and tricuspid insufficiency and no sign of tuberous sclerosis. She was successfully treated with an operation, the treatment plan included mass resection, tricuspid annuloplasty, and closure of the patent foramen ovale. The right atrial lesion was resected entirely, while the lobulated lesion in the right ventricle was resected as two pieces. There was no evidence of recurrence 1 year after the surgery.
原发性心脏肿瘤非常罕见，通常为良性。最常见的类型是心脏横纹肌瘤，占原发性心脏肿瘤的45%至75%。心脏横纹肌瘤是一种罕见的良性肿瘤，常与结节性硬化症相关。我们报告一例患有多灶性心脏横纹肌瘤、房间隔缺损和三尖瓣关闭不全且无结节性硬化症迹象的婴儿病例。她通过手术成功治疗，治疗方案包括肿块切除、三尖瓣成形术和卵圆孔未闭封堵术。右心房病变被完全切除，而右心室的分叶状病变被切成两块切除。术后1年无复发迹象。
