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拉斯穆森脑炎:一例报告。

Rasmussen's encephalitis: A case report.

作者信息

Vimal Joseph, Nagarajan Ramesh, Sriram Deepika

机构信息

Department of Internal Medicine, Pondicherry Institute of Medical Sciences, Pondicherry, India.

出版信息

Australas Med J. 2015 Mar 31;8(3):80-4. doi: 10.4066/AMJ.2015.2255. eCollection 2015.

DOI:10.4066/AMJ.2015.2255
PMID:25870657
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4385812/
Abstract

Rasmussen's encephalitis (RE) is a rare neurological disorder of inflammatory aetiology characterised by encephalitis, intractable seizures, hemiparesis, variable motor deficits, and dementia. It is not commonly considered in the clinical differential diagnosis of a patient with a past history of a stroke-like episode presenting with status epilepticus. It is suspected mainly in children in whom the disease is more common. Here we report a case of an adult man presenting with a common symptom of seizure caused by Rasmussen's encephalitis.

摘要

拉斯穆森脑炎(RE)是一种病因不明的罕见神经系统炎性疾病,其特征为脑炎、顽固性癫痫、偏瘫、不同程度的运动功能障碍和痴呆。对于有类似中风发作病史且伴有癫痫持续状态的患者,在临床鉴别诊断中通常不会考虑到该病。主要在儿童中怀疑患有此病,因为该疾病在儿童中更为常见。在此,我们报告一例成年男性因拉斯穆森脑炎出现癫痫这一常见症状的病例。

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本文引用的文献

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Rasmussen encephalitis: incidence and course under randomized therapy with tacrolimus or intravenous immunoglobulins.拉森脑炎:在他克莫司或静脉注射免疫球蛋白随机治疗下的发生率和病程。
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Advances in pathogenic concepts and therapeutic agents in Rasmussen's encephalitis.
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