Ahamed Syed Kowsar, Al-Thobaiti Yasser
Assistant Consultant, Department of Maxillofacial Surgery, King Abdullah Medical City, Makkah, Saudi Arabia.
Swedish Board, Consultant, Department of Maxillofacial Surgery, Abdullah Medical Center, Makkah, Saudi Arabia; Assistant Professor, Consultant, Department of Oral & Maxillofacial Surgery, Faculty of Dentistry, Taif University, Taif, Saudi Arabia.
J Oral Maxillofac Surg. 2015 Aug;73(8):1465.e1-5. doi: 10.1016/j.joms.2015.03.043. Epub 2015 Mar 21.
Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant disorder of fibrovascular tissues. Patients with HHT often develop life-threatening bleeds from telangiectasias in the nasal or gastrointestinal mucosa or from visceral arteriovenous malformations. Recurrent oral bleeds are rare presentations in these patients and are seldom reported. This report describes a rare case of 72-year-old man with a known history of HHT who presented with a recurrent life-threatening oral bleed from telangiectasia of the palate and reviews the literature for current trends of medical and dental management. This study is an effort to draw the attention of oral physicians and surgeons to such drastic complications of the disease and various current treatment modalities.
遗传性出血性毛细血管扩张症（HHT）是一种常染色体显性遗传性纤维血管组织疾病。HHT患者常因鼻腔或胃肠道黏膜的毛细血管扩张或内脏动静脉畸形而发生危及生命的出血。复发性口腔出血在这些患者中较为罕见，报道也很少。本报告描述了一例罕见病例，一名72岁男性，有HHT病史，因腭部毛细血管扩张出现复发性危及生命的口腔出血，并回顾了关于当前医学和牙科治疗趋势的文献。本研究旨在引起口腔内科医生和外科医生对该疾病此类严重并发症及各种当前治疗方式的关注。
