Goo Hyun Woo, Ra Young-Shin
Department of Radiology and Research Institute of Radiology, and.
Department of Neurosurgery, University of Ulsan College of Medicine, Asan Medical Center, Seoul, South Korea.
J Neurosurg Pediatr. 2015 Jul;16(1):50-3. doi: 10.3171/2014.12.PEDS14609. Epub 2015 Apr 17.
Medullary hemangioblastoma is very rare in children. Based on small nodular enhancement with peritumoral edema and without dilated feeding arteries on conventional MRI, hemangioblastoma, pilocytic astrocytoma, oligodendroglioma, and ganglioglioma were included in the differential diagnosis of the medullary tumor. In this case report, the authors emphasize the diagnostic value of arterial spin labeling and dynamic contrast-enhanced MRI in demonstrating vascular tumor perfusion of hemangioblastoma in a 12-year-old boy who was later found to have von Hippel-Lindau disease.
髓质血管母细胞瘤在儿童中非常罕见。基于常规MRI上的小结节强化、瘤周水肿且无扩张的供血动脉,血管母细胞瘤、毛细胞型星形细胞瘤、少突胶质细胞瘤和神经节胶质瘤被纳入髓质肿瘤的鉴别诊断。在本病例报告中,作者强调了动脉自旋标记和动态对比增强MRI在一名12岁男孩血管母细胞瘤血管肿瘤灌注显示中的诊断价值,该男孩后来被发现患有冯·希佩尔-林道病。