Joliat Gaëtan-Romain, Melloul Emmanuel, Djafarrian Reza, Schmidt Sabine, Fontanella Sara, Yan Pu, Demartines Nicolas, Halkic Nermin
Division of Visceral Surgery, University Hospital CHUV, Rue du Bugnon 46, 1011, Lausanne, Vaud, CH, Switzerland.
Department of Radiology, University Hospital CHUV, Lausanne, Switzerland.
World J Surg Oncol. 2015 Feb 15;13:58. doi: 10.1186/s12957-015-0490-0.
Cystic lymphangioma is a rare tumor of the lymphatic vessels that occurs more frequently in women. Location of this pathology can be diverse but most commonly occurs in the neck or axilla. Cystic lymphangioma originating from the adrenal tissue represents a very rare entity.
We report here the case of a 38-year-old woman who was diagnosed with a cystic retroperitoneal mass. After further investigations, the patient was suspected to have a left adrenal cystic lymphangioma. She underwent successful open left adrenalectomy as curative treatment, and the diagnosis of cystic lymphangioma of the left adrenal gland was confirmed at histology. The postoperative course was uneventful.
This case report and review of the literature bring new insights into the diagnostic difficulty and management of cystic lymphangioma of the adrenal gland.
囊性淋巴管瘤是一种罕见的淋巴管肿瘤,在女性中更为常见。这种病变的位置可以多种多样,但最常见于颈部或腋窝。起源于肾上腺组织的囊性淋巴管瘤是一种非常罕见的实体。
我们在此报告一例38岁女性,她被诊断为腹膜后囊性肿块。经过进一步检查,怀疑该患者患有左肾上腺囊性淋巴管瘤。她接受了成功的开放性左肾上腺切除术作为根治性治疗,组织学检查证实为左肾上腺囊性淋巴管瘤。术后过程顺利。
本病例报告及文献复习为肾上腺囊性淋巴管瘤的诊断困难和治疗带来了新的见解。