Saravakos Panagiotis, Hartwein Joerg, Fayyazi Afshin
Department of Otolaryngology, Head and Neck Surgery, Siloah St. Trudpert Hospital, Pforzheim, Germany.
Institute of Pathology and Molecular Pathology, Pforzheim Hospital, Pforzheim, Germany.
Head Neck. 2016 Jan;38(1):E13-5. doi: 10.1002/hed.24084. Epub 2015 Jul 18.
Sialoblastoma is an extremely rare congenital salivary gland tumor of epithelial origin. It is usually localized in the parotid or submandibular gland and presents primarily at birth or in early childhood.
We report a case of a 13-year-old girl with a sialoblastoma of the parotid gland presenting as an asymptomatic painless mass.
The patient showed multiple recurrences and, based on the histopathological finding of facial nerve infiltration, was treated surgically with total parotidectomy and facial nerve reconstruction.
Because of the rare occurrence of sialoblastoma, there is no evidence-based treatment of choice. The treatment should be individualized, taking into consideration the patient's age, the high locoregional recurrence rate, the local aggressive characteristics, and the potential metastatic activity of this rare tumor. A close follow-up of the patient is strongly recommended.
涎母细胞瘤是一种极其罕见的先天性上皮源性涎腺肿瘤。它通常位于腮腺或下颌下腺，主要在出生时或儿童早期出现。
我们报告一例13岁女孩，患有腮腺涎母细胞瘤，表现为无症状的无痛性肿块。
该患者出现多次复发，基于面神经浸润的组织病理学发现，接受了全腮腺切除术及面神经重建手术治疗。
由于涎母细胞瘤的罕见性，尚无基于证据的治疗选择。治疗应个体化，考虑患者年龄、高局部区域复发率、局部侵袭性特征以及这种罕见肿瘤的潜在转移活性。强烈建议对患者进行密切随访。
