Klusmeier Elmar, Haas Nikolaus A, Sandica Eugen
1Department for Pediatric Cardiology/Congenital Heart Defects,Centre for Congenital Heart Defects,Heart and Diabetes Centre North-Rhine Westfalia,Germany.
2Department of Surgery for Congenital Heart Defects,Heart and Diabetes Centre North-Rhine Westfalia,Germany.
Cardiol Young. 2016 Jan;26(1):194-6. doi: 10.1017/S1047951115000414. Epub 2015 Apr 30.
Truncus arteriosus communis is a rare CHD, accounting for only 1% of all congenital cardiac abnormalities. It has been associated with other malformations of the heart, mainly truncal valve (bicuspid/quadricuspid) and aortic arch abnormalities such as right, interrupted, and hypoplastic aortic arch. Cor tratriatrum sinistrum is another rare CHD, and it has been associated with other cardiac defects such as anomalous pulmonary venous drainage, ventricular septal defect, coarctation of the aorta, and tetralogy of Fallot. The combination of truncus arteriosus communis and cor tratriatrum sinistrum has not been reported so far. This case study describes the diagnosis of a unique case, including these two very rare cardiac defects and the successful surgical treatment thereafter.
共同动脉干是一种罕见的先天性心脏病,仅占所有先天性心脏畸形的1%。它与其他心脏畸形有关,主要是动脉干瓣膜(二叶/四叶)和主动脉弓异常,如右位主动脉弓、中断主动脉弓和发育不全主动脉弓。左房三房心是另一种罕见的先天性心脏病,它与其他心脏缺陷有关,如肺静脉异位引流、室间隔缺损、主动脉缩窄和法洛四联症。共同动脉干和左房三房心的组合迄今尚未见报道。本病例研究描述了一例独特病例的诊断,包括这两种非常罕见的心脏缺陷以及随后的成功手术治疗。