Hussain Niaz, Naveed Mujtaba Zaki, Haider Ghulam
Ojha Institute of Chest Disease and Dow University Hospital, Karachi, Pakistan.
Aga Khan University Hospital, Karachi, Pakistan.
J Pak Med Assoc. 2015 Mar;65(3):324-6.
Dermatofibrosarcomaprotuberans is a rare, soft tissue tumour with high rate of recurrence. It is locally aggressive, with a low rate of metastasis. We describe the case of a 42 year old man who presented with a re-recurrent, large tumour situated on the anterior chest wall in the sternal region. We did a wide local excision and covered the resulting defect by using bilateral, pectoralis major myocutaneous flaps. Histopathology and immunohistochemical staining findings were consistent with the diagnosis of Dermatofibrosarcoma Protuberance. Post operatively the patient was treated with chemotherapy and radiotherapy.
隆突性皮肤纤维肉瘤是一种罕见的软组织肿瘤，复发率高。它具有局部侵袭性，转移率低。我们描述了一名42岁男性的病例，该患者胸骨区前胸壁出现复发性大肿瘤。我们进行了广泛的局部切除，并使用双侧胸大肌肌皮瓣覆盖由此产生的缺损。组织病理学和免疫组化染色结果与隆突性皮肤纤维肉瘤的诊断一致。术后患者接受了化疗和放疗。
