Kordač Petr, Nikolov Dimitar Hadži, Smatanová Katarína, Kalfeřt David
Department of Otorhinolaryngology and Head and Neck Surgery, University Hospital Hradec Králové, Charles University in Prague, Faculty of Medicine in Hradec Králové, Czech Republic.
The Fingerland Department of Pathology, University Hospital Hradec Králové, Charles University in Prague, Faculty of Medicine in Hradec Králové, Czech Republic.
Acta Medica (Hradec Kralove). 2014;57(4):162-4. doi: 10.14712/18059694.2015.82.
Low-grade myofibroblastic sarcoma (LGMS) is a very rare, atypical myofibroblastic tumor with fibromatosis-like features with predilection mostly in head and neck region. LGMS occurs primarily in adult patients with a slight male predominance. Only few cases of LGMS affecting the larynx have been reported in literature to this date. We describe a case of low-grade myofibroblastic sarcoma of the larynx in a 40-year-old male patient. The clinicopathological characteristics, immunohistochemical findings and treatment are discussed.
低度恶性肌成纤维细胞肉瘤(LGMS)是一种非常罕见的非典型肌成纤维细胞肿瘤,具有纤维瘤病样特征,主要好发于头颈部区域。LGMS主要发生于成年患者,男性略占优势。迄今为止,文献中仅报道了少数几例累及喉部的LGMS病例。我们描述了一例40岁男性患者的喉部低度恶性肌成纤维细胞肉瘤病例。并对其临床病理特征、免疫组化结果及治疗进行了讨论。