Department of Obstetrics and Gynecology, The University of Texas Medical Branch at Galveston, Galveston, TX.
J Low Genit Tract Dis. 1999 Apr;3(2):135-8. doi: 10.1046/j.1526-0976.1999.08100.x.
Dermatofibrosarcoma protuberans (DFSP), a low-grade sarcoma of dermal origin, rarely is found on the vulva. Only 16 cases of DFSP of the vulva have been described.
Two patients with long histories of primary vulvar dermatofibrosarcoma protuberans are presented. Both required multiple excisions to resect the tumor completely. The patients remain without evidence of disease after long-term follow-up. One patient is among the youngest recorded. All published cases of vulvar DFSP are reviewed.
Both our experience and that reported in previous cases indicate that wide local excision is required in the treatment of vulvar DFSP.
隆突性皮肤纤维肉瘤（DFSP），一种源自真皮的低度恶性肉瘤，很少发生在女性外阴。仅描述了 16 例外阴 DFSP 病例。
介绍了 2 例有长期原发性外阴隆突性皮肤纤维肉瘤病史的患者。均需要多次切除才能彻底切除肿瘤。长期随访后，患者均无疾病证据。其中 1 例患者为记录中年龄最小者。回顾所有已发表的外阴 DFSP 病例。
我们的经验和以往病例报告均表明，广泛局部切除是治疗外阴 DFSP 的必要手段。
