Das Bibhuti B
Division of Pediatric Cardiology, Department of Pediatrics, Children's Medical Center, UT Southwestern Medical Center, 1935 Medical District Dr, Dallas, TX, 75235, USA,
Pediatr Cardiol. 2015 Aug;36(6):1120-8. doi: 10.1007/s00246-015-1184-7. Epub 2015 May 10.
The Eisenmenger syndrome (ES) is a severe form of pulmonary arterial hypertension and arises in congenital heart disease with a systemic-to-pulmonary shunt. Patients with ES have multisystem involvement as a result of chronic hypoxemia with hematologic, skeletal, renal, and neurologic systems, causing significant morbidity and mortality. In contrast to pulmonary arterial hypertension, survival prospects are far superior in patients with ES and a growing number of ES patients are surviving into adulthood. As a result, many face the prospect of incidental surgery. To date, there is no guideline for the perioperative care of ES patients in children and limited data available for adult patients. This review provides an overview of appropriate measures for the safe perioperative care of patients, based on an understanding of the pathophysiological changes that occur in ES.
艾森曼格综合征（ES）是一种严重的肺动脉高压形式，发生于先天性心脏病合并体循环至肺循环分流的患者。ES患者由于慢性低氧血症累及血液、骨骼、肾脏和神经系统，出现多系统受累，导致显著的发病率和死亡率。与肺动脉高压不同，ES患者的生存前景要好得多，越来越多的ES患者存活至成年。因此，许多患者面临着意外手术的可能性。迄今为止，尚无关于儿童ES患者围手术期护理的指南，针对成年患者的可用数据也有限。基于对ES患者发生的病理生理变化的理解，本综述概述了对患者进行安全围手术期护理的适当措施。
