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肾细胞癌与无肌病性皮肌炎。

Renal cell carcinoma and amyopathic dermatomyositis.

作者信息

Adili Anthony F, Liaconis Haralambos, Gusenbauer Kaela, Kapoor Anil

机构信息

Section of Urology, Department of Surgery, McMaster University, Hamilton, ON.

出版信息

Can Urol Assoc J. 2015 May-Jun;9(5-6):E340-2. doi: 10.5489/cuaj.2362.

Abstract

Amyopathic dermatomyositis (dermatomyositis siné myositis) is a rare disorder with cutaneous lesions identical to those of classic dermatomyositis, but with no clinical evidence of myopathy. Association with malignancy has been suggested in a number of reports. We report the case of a 69-year-old man with a recent diagnosis of amyopathic dermatomyositis, who presented to the urology service with hematuria. Investigations revealed a 5.8-cm renal cell carcinoma and the patient underwent left radical nephrectomy without complication. To our knowledge, an association with renal cell carcinoma and amyopathic dermatomyositis has not been previously described.

摘要

无肌病性皮肌炎(无肌性皮肌炎)是一种罕见的疾病,其皮肤损害与典型皮肌炎相同,但无肌病的临床证据。一些报告提示其与恶性肿瘤有关。我们报告一例69岁男性,近期诊断为无肌病性皮肌炎,因血尿就诊于泌尿外科。检查发现一个5.8厘米的肾细胞癌,患者接受了左肾根治性切除术,无并发症。据我们所知,此前尚未描述过肾细胞癌与无肌病性皮肌炎之间的关联。

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