Jamshidi Khodamorad, Najd Mazhar Farid, Jafari Davod
Bone and Joint Reconstruction Research Center, Shafa Yahyaeian hospital, Iran University of Medical Sciences, Tehran, Iran.
Bone and Joint Reconstruction Research Center, Shafa Yahyaeian hospital. Iran University of Medical Sciences, Tehran, Iran.
Arch Iran Med. 2015 Jun;18(6):367-70.
Chondromyxoid fibroma is a rare benign primary bone tumor of cartilaginous origin, which most commonly involves the metaphyseal bone of proximal tibia and distal femur. The purpose of the study is to report our experience with diagnosis and surgical management of Chondromyxoid fibroma in the pelvic region.
Eight consecutive patients with a final diagnosis of pelvic Chondromyxoid fibroma were treated from 2001 to 2010. We considered the presentations and outcome for surgical complications and local recurrence after extended curettage and allogenic corticocancellous bone grafting.
Three patients were female and five were male. The median follow up period was 72 (30-126) months. The mean age of cases was 31.9 (20-41) years. Five patients had left side involvement and in the remaining three, the right side was involved. Four involved periacetabulum, two involved the ilium and the remaining two cases were ischiopubic. The mean Musculoskeletal Tumor Society Score was 94.1%. The major complications were recurrence in one case and herniation after pubic rami resection in another case.
Chondromyxoid fibroma should be distinguished from chondrosarcoma. Management recommendation includes extensive curettage and corticocancellous bone grafting. We also advocate use of fibular strut allograft for reconstruction of pubic rami after its resection to prevent hernia in cases with pubic rami involvement.
软骨黏液样纤维瘤是一种罕见的起源于软骨的原发性良性骨肿瘤，最常累及胫骨近端和股骨远端的干骺端骨。本研究的目的是报告我们在盆腔区域软骨黏液样纤维瘤诊断和手术治疗方面的经验。
2001年至2010年，连续治疗了8例最终诊断为盆腔软骨黏液样纤维瘤的患者。我们考虑了扩大刮除术和同种异体皮质松质骨移植术后的手术并发症和局部复发情况及结果。
3例为女性，5例为男性。中位随访期为72（30 - 126）个月。病例的平均年龄为31.9（20 - 41）岁。5例累及左侧，其余3例累及右侧。4例累及髋臼周围，2例累及髂骨，其余2例为耻骨坐骨支受累。肌肉骨骼肿瘤学会平均评分为94.1%。主要并发症为1例复发，另1例耻骨支切除术后出现疝。
软骨黏液样纤维瘤应与软骨肉瘤相鉴别。治疗建议包括广泛刮除术和皮质松质骨移植。我们还主张在耻骨支受累的病例中，在耻骨支切除后使用腓骨支撑异体骨进行重建以预防疝。
