Burns A M, Shelly M P
Shackelton Department of Anaesthetics, Southampton General Hospital.
Anaesthesia. 1989 Dec;44(12):975-7. doi: 10.1111/j.1365-2044.1989.tb09200.x.
The anaesthetic management for an infant with mitochondrial encephalomyopathy due to fumarase deficiency is described. Mitochondrial myopathies may produce skeletal and cardiac muscle abnormalities, central nervous system effects and metabolic problems. The solutions to the anaesthetic problems posed by these patients are discussed.
本文描述了对一名因富马酸酶缺乏导致线粒体脑肌病的婴儿的麻醉管理。线粒体肌病可能会导致骨骼肌和心肌异常、中枢神经系统影响以及代谢问题。文中讨论了这些患者所带来的麻醉问题的解决方法。