Murakami T, Dixon A C, Ho R C, Nakamura J M
Hawaii Med J. 1989 Oct;48(10):430-2, 434-6.
Extramedullary hematopoiesis (EMH) is observed in people suffering from severe anemia of prolonged duration and appears to be a compensatory mechanism for disturbed medullary hematopoiesis. The hemoglobinopathies (such as thalassemia, spherocytosis, and sickle cell disease), neoplastic diseases such as leukemia and lymphoma, and others, including myelofibrosis and osteitis fibrosa cystica, are associated with EMH. These diseases and their resultant anemia have in common the ability to stimulate erythropoietin production, which in turn may stimulate hematopoiesis in organs of mesenchymal origin. The liver and spleen are the most common sites of EMH; however, other sites, including the falx cerebri, thoracic cavity, retroperitoneal area and pelvis have been reported. When present, intrathoracic EMH is most frequently associated with thalassemia. Spinal cord compression and hemothorax have also been reported as complications of intrathoracic EMH.
髓外造血(EMH)见于患有长期严重贫血的人群,似乎是骨髓造血功能紊乱的一种代偿机制。血红蛋白病(如地中海贫血、球形红细胞增多症和镰状细胞病)、白血病和淋巴瘤等肿瘤性疾病,以及其他疾病,包括骨髓纤维化和囊性纤维性骨炎,均与髓外造血有关。这些疾病及其导致的贫血共同具有刺激促红细胞生成素产生的能力,这反过来又可能刺激间充质来源器官的造血。肝脏和脾脏是髓外造血最常见的部位;然而,其他部位,包括大脑镰、胸腔、腹膜后区域和骨盆也有相关报道。胸腔内髓外造血一旦出现,最常与地中海贫血相关。脊髓压迫和血胸也被报道为胸腔内髓外造血的并发症。