Lopez-Oliva Clarissa Linda Liboro, Wang Edward H M, Cañal Johanna Patricia A
Musculoskeletal Tumour Service, Department of Orthopaedics, University of the Philippines-Philippine General Hospital, Ermita, Manila, Philippines.
Department of Radiology, University of the Philippines-Philippine General Hospital, Ermita, Manila, Philippines.
Int Orthop. 2015 Oct;39(10):2037-40. doi: 10.1007/s00264-015-2930-4. Epub 2015 Jul 31.
Synovial haemangioma is a rare type of tumour for which only around 200 cases have been reported worldwide. It usually occurs in the female population during the second decade of life and most commonly affects the knee joint. Patients can complain of pain, recurrent knee swelling and limitation of motion. Since these lesions are uncommon and radilogical findings are nonspecific, physician awareness is low and diagnosis is often delayed, leading in turn to treatment delays and irreversible complications of the affected joint.
We report four cases of synovial haemangioma of the knee seen over a period of 20 years (1993-2013). Age at presentation ranged from six to 43 years (mean of 22.7 years) with an equal male-to-female ratio. Average duration of symptoms prior to treatment was three years--patients were often misdiagnosed and appropriate treatment was subsequently delayed. Radiographs showed moderate to severe degenerative changes. Magnetic resonance (MR) imaging revealed poorly defined intra-articular contrast-enhancing lesions, all of which were of the localised type. Three patients underwent open synovectomy and en bloc excision of the lesion; the fourth deferred surgery but continues to be monitored. Follow-up ranged from one to 11 years; all four patients are doing well, with no signs of symptom recurrence or progression.
Synovial haemangioma is a rare but treatable condition. It should remain a differential for any patient with recurrent knee-joint symptoms.
滑膜血管瘤是一种罕见的肿瘤类型,全球仅报道了约200例。它通常发生于青春期女性,最常累及膝关节。患者可出现疼痛、膝关节反复肿胀及活动受限。由于这些病变不常见且影像学表现不具特异性,医生对此认识不足,诊断常被延误,进而导致治疗延迟及受累关节出现不可逆并发症。
我们报告了20年间(1993 - 2013年)所见的4例膝关节滑膜血管瘤。就诊时年龄为6至43岁(平均22.7岁),男女比例相同。治疗前症状平均持续时间为3年——患者常被误诊,随后适当治疗被延误。X线片显示中度至重度退行性改变。磁共振成像显示关节内边界不清的强化病变,均为局限性类型。3例患者接受了开放性滑膜切除术及病变整块切除术;第4例推迟手术但仍在接受监测。随访时间为1至11年;所有4例患者情况良好,无症状复发或进展迹象。
滑膜血管瘤虽罕见但可治疗。对于任何有膝关节反复症状的患者,都应将其列为鉴别诊断之一。