卡-恩二氏病中的双侧视乳头水肿
Bilateral papilloedema in Camurati-Engelmann disease.
作者信息
Popiela Magdalena, Austin Michael
机构信息
Abertawe Bro Morgannwg University Health Board, Singleton Hospital, Swansea, UK.
出版信息
BMJ Case Rep. 2015 Aug 18;2015:bcr2014207348. doi: 10.1136/bcr-2014-207348.
Abstract
A 23-year-old woman presented with bilateral papilloedema in a setting of Camurati-Engelmann disease (CED). She was investigated with neuroimaging showing no optic nerve canal stenosis or jugular vein canal compromise. Her MRI venogram was normal. Her opening pressure at lumbar puncture and serum alkaline phosphatase were raised. Her papilloedema resolved with long-term use of acetazolamide. We believe that our patient suffered from raised intracranial pressure directly as a result of decreasing intracranial volume secondary to CED.
摘要
一名23岁女性在卡穆拉蒂-恩格尔曼病（CED）背景下出现双侧视乳头水肿。对她进行了神经影像学检查，结果显示没有视神经管狭窄或颈静脉管受压。她的磁共振静脉血管造影正常。她腰椎穿刺时的初压及血清碱性磷酸酶升高。长期使用乙酰唑胺后她的视乳头水肿消退。我们认为，我们的患者颅内压升高直接是由于CED导致颅内容积减小所致。
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