多骨型纤维发育不良伴发肌内黏液瘤：马扎布罗德综合征。

Polyostotic fibrous dysplasia associated with intramuscular myxomas: Mazabraud syndrome.

作者信息

Samper Wamba Jose Daniel, Fernandez Bermudez Maria Jose, Dominguez Teresa Lorenzo, Pascua Luis Ramos

机构信息

Department of Radiology, University Hospital of León, León, Spain.

Department of Orthopaedics and Traumatology, University Hospital of León, León, Spain.

出版信息

Indian J Radiol Imaging. 2015 Jul-Sep;25(3):280-3. doi: 10.4103/0971-3026.161456.

DOI:10.4103/0971-3026.161456

PMID:26288523

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4531453/

Abstract

The authors report a new case of Mazabraud syndrome in a 69-year-old woman complaining of pain in her right thigh. Plain radiographs demonstrated radiological findings consistent with polyostotic fibrous dysplasia of the right femur and tibia. Magnetic resonance imaging (MRI) study showed soft tissue tumors located in the vastus intermedius muscle with typical signal features of intramuscular myxomas. Biopsy was not performed because of its benign nature. Symptomatic treatment was prescribed and all the lesions remained 1 year after the diagnosis.

摘要

作者报告了一例69岁女性马扎布罗综合征新病例，该患者主诉右大腿疼痛。X线平片显示的影像学表现与右股骨和胫骨的多骨型纤维发育异常相符。磁共振成像（MRI）研究显示位于股中间肌的软组织肿瘤，具有肌内黏液瘤的典型信号特征。由于其良性性质，未进行活检。给予了对症治疗，诊断后1年所有病变均持续存在。