João S R, Afonso M R, Martins Júnior L, Almeida Júnior B N, Simões R P, França H H
Arq Bras Cardiol. 1989 Oct;53(4):221-3.
The study concerns a 44 year-old male patient with a history of intermittent episodes of rheumatic activity; the physical examination showed mitral valve stenosis and metacarpophalangeal joint deformities. The joint deformities were bilateral and symmetrical, similar to that of rheumatoid arthritis. Nevertheless, the ulnar deviation of the hands was reversible and there were no typical signs of rheumatoid arthritis in the X-ray. In view of the facts, the diagnosis of Jaccoud's Artrhopathy (JA) was made. The pathogenesis, the clinical features and the association between mitral valve stenosis and joints deformities of JA are discussed. This disease has a good prognosis and it is sparsely mentioned in the cardiologic literature. Many patients with JA are diagnosed as having rheumatoid arthritis, which is a chronic and disabling disease.
该研究涉及一名44岁男性患者,有风湿活动间歇性发作病史;体格检查显示二尖瓣狭窄和掌指关节畸形。关节畸形为双侧对称,与类风湿关节炎相似。然而,手部尺侧偏斜是可逆的,X线检查无类风湿关节炎的典型征象。鉴于这些事实,诊断为雅各布关节病(JA)。文中讨论了JA的发病机制、临床特征以及二尖瓣狭窄与关节畸形之间的关联。这种疾病预后良好,在心脏病学文献中很少提及。许多JA患者被诊断为患有类风湿关节炎,而类风湿关节炎是一种慢性致残性疾病。