Bensaid Badr, Khalil Jihane, Ould Salek Elhadj, El Khaloufi Samir, Elidrissi Redouane, Lekehal Brahim, Sefyani Yassir, Elmesnaoui Abbas, Benjaafar Noureddine, Bensaid Younes
Vascular Surgery Department, Avycenn Hospital, Mohamed V University, Rabat, Morocco.
Radiation Oncology Department, National Institute of Oncology, Mohamed V University, Rabat, Morocco.
Ann Vasc Surg. 2015 Nov;29(8):1661.e9-15. doi: 10.1016/j.avsg.2015.06.086. Epub 2015 Aug 24.
Paragangliomas are neuroendocrine tumors derived from the extra-adrenal paraganglia of the autonomic nervous system. Only 3% of all paragangliomas are reported to occur in the head and neck region. The most common paraganglioma of the head and neck is the carotid body tumor. Only few cases have been described in the literature regarding the pediatric age group less than aged 14 years, mostly as case reports.
Our case describes a massive paraganglioma in the head and neck region occurring in a 3-year-old Arabic boy, for which surgical excision was not possible and radiotherapy resulted in a good clinical and radiologic response.
Paragangliomas a rare in children and mostly diagnosed in a locally advanced stage. Surgery in most cases is difficult especially because of the proximity of the vessels; radiotherapy is still a good alternative for those cases.
副神经节瘤是起源于自主神经系统肾上腺外副神经节的神经内分泌肿瘤。据报道，所有副神经节瘤中仅有3%发生于头颈部区域。头颈部最常见的副神经节瘤是颈动脉体瘤。关于14岁以下儿童年龄组的病例，文献中仅有少数描述，大多为病例报告。
我们的病例描述了一名3岁阿拉伯男孩头颈部发生的巨大副神经节瘤，无法进行手术切除，放疗取得了良好的临床和影像学反应。
副神经节瘤在儿童中罕见，大多在局部晚期被诊断出来。在大多数情况下，手术困难，尤其是因为血管位置临近；对于这些病例，放疗仍是一种不错的选择。
