Abdelhady Khaled, Durgam Samarth, Orza Daniela, Massad Malek G
Division of Cardiothoracic Surgery, University of Illinois, Chicago, Illinois.
Division of Cardiothoracic Surgery, University of Illinois, Chicago, Illinois.
Ann Thorac Surg. 2017 Apr;103(4):e323-e325. doi: 10.1016/j.athoracsur.2016.09.062.
We report a rare case of left atrial paraganglioma with a synchronous carotid body paraganglioma in a 30-year-old man with succinate dehydrogenase B gene mutation. The patient initially presented with a neck mass and palpitations. Laboratory test results showed elevated catecholamine levels. A cardiac paraganglioma was identified by computed tomography, meta-iodobenzylguanidine scintigraphy, and magnetic resonance imaging. Surgical resection of both paragangliomas were performed on two separate occasions. Serum and urine catecholamine levels returned to normal range. On follow-up, there was no recurrence of the cardiac paraganglioma. Radiotherapy was subsequently initiated for recurrence in the carotid body paraganglioma.
我们报告了一例罕见的左心房副神经节瘤病例，该患者为一名30岁男性，同时患有颈动脉体副神经节瘤，伴有琥珀酸脱氢酶B基因突变。患者最初表现为颈部肿块和心悸。实验室检查结果显示儿茶酚胺水平升高。通过计算机断层扫描、间碘苄胍闪烁显像和磁共振成像确定了心脏副神经节瘤。两次分别对两个副神经节瘤进行了手术切除。血清和尿儿茶酚胺水平恢复到正常范围。随访时，心脏副神经节瘤未复发。随后对颈动脉体副神经节瘤的复发开始进行放射治疗。
