高苯丙氨酸血症中的微量营养素。
Micronutrient in hyperphenylalaninemia.
作者信息
Crujeiras Vanesa, Aldámiz-Echevarría Luís, Dalmau Jaume, Vitoria Isidro, Andrade Fernando, Roca Iria, Leis Rosaura, Fermandez-Marmiesse Ana, Couce María L
机构信息
Unit of Gastroenterology and Nutrition, Department of Pediatrics, Hospital Clinico Universitario de Santiago, Travesía da Choupana s/n, 15706 Santiago de Compostela, A Coruña, Spain.
Unit of Metabolism, Department of Pediatrics, Hospital de Cruces, Group of Metabolism, Biocruces Health Research Institute, CIBERER, Plaza de Cruces s/n, 48903 Barakaldo, Vizcaya, Spain.
出版信息
Data Brief. 2015 Aug 1;4:614-21. doi: 10.1016/j.dib.2015.07.026. eCollection 2015 Sep.
The data presented here are the biochemical parameters of 156 patients with hyperphenylalaninemia. PKU patients, who, in order to maintain optimal serum Phe concentrations, receive dietary treatment consisting of a diet low in natural protein supplemented with special low protein foods and a Phe-free amino acid mixture, vitamins and minerals. The obtained data reflects a high percentage of patients with prealbumin and selenium deficiencies, as well as an increased level of folic acid. This data article is related to the research article entitled, "Vitamin and mineral status in patients with hyperphenylalaninemia", by Crujeiras et al. [1].
此处呈现的数据是156例高苯丙氨酸血症患者的生化参数。苯丙酮尿症（PKU）患者为维持最佳血清苯丙氨酸（Phe）浓度，接受饮食治疗，该治疗包括低天然蛋白饮食，并补充特殊的低蛋白食品以及无Phe的氨基酸混合物、维生素和矿物质。所获得的数据反映出高比例的患者存在前白蛋白和硒缺乏，以及叶酸水平升高。本数据文章与Crujeiras等人发表的题为《高苯丙氨酸血症患者的维生素和矿物质状况》的研究文章相关[1]。
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