脆性X综合征患儿的适应性行为会出现下降或停滞吗？
Do Children With Fragile X Syndrome Show Declines or Plateaus in Adaptive Behavior?
作者信息
Hahn Laura J, Brady Nancy C, Warren Steven F, Fleming Kandace K
出版信息
Am J Intellect Dev Disabil. 2015 Sep;120(5):412-32. doi: 10.1352/1944-7558-120.5.412.
Abstract
This study explores if children with fragile X syndrome (FXS) show advances, declines, or plateaus in adaptive behavior over time and the relationship of nonverbal cognitive abilities and autistic behavior on these trajectories. Parents of 55 children with FXS completed the Vineland Adaptive Behavior Scales ( Sparrow, Balla, & Cicchetti, 1984 ; Sparrow, Cicchetti, & Balla, 2005 ) between 3 and 6 times from 2 to 10 years of age. Using raw scores, results indicate that about half of the sample showed advances in adaptive behavior, whereas the other half showed declines, indicating a regression in skills. Children who were more cognitively advanced and had less autistic behaviors had higher trajectories. Understanding the developmental course of adaptive behavior in FXS has implications for educational planning and intervention, especially for those children showing declines.
摘要
本研究探讨脆性X综合征（FXS）患儿的适应性行为随时间推移是进步、衰退还是停滞，以及非言语认知能力和自闭症行为在这些轨迹上的关系。55名FXS患儿的家长在孩子2至10岁期间，3至6次完成了文兰适应性行为量表（斯帕罗、巴拉和西凯蒂，1984年；斯帕罗、西凯蒂和巴拉，2005年）。使用原始分数，结果表明约一半的样本在适应性行为方面有进步，而另一半则出现衰退，表明技能出现倒退。认知能力较强且自闭症行为较少的儿童有更高的轨迹。了解FXS患儿适应性行为的发展过程对教育规划和干预具有重要意义，特别是对于那些出现衰退的儿童。
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