Rosales Ivy A, Collins A Bernard, do Carmo Paula Alves S, Tolkoff-Rubin Nina, Smith R Neal, Colvin Robert B
Department of Pathology and
Department of Pathology and.
J Am Soc Nephrol. 2016 Feb;27(2):380-4. doi: 10.1681/ASN.2015030334. Epub 2015 Sep 2.
Immune complex tubulointerstitial nephritis due to antibodies to brush border antigens of the proximal tubule has been demonstrated experimentally and rarely in humans. Our patient developed ESRD and early recurrence after transplantation. IgG and C3 deposits were conspicuous in the tubular basement membrane of proximal tubules, corresponding to deposits observed by electron microscopy. Rare subepithelial deposits were found in the glomeruli. The patient had no evidence of SLE and had normal complement levels. Serum samples from the patient reacted with the brush border of normal human kidney, in contrast with the negative results with 20 control serum samples. Preliminary characterization of the brush border target antigen excluded megalin, CD10, and maltase. We postulate that antibodies to brush border antigens cause direct epithelial injury, accumulate in the tubular basement membrane, and elicit an interstitial inflammatory response.
实验已证实,由针对近端肾小管刷状缘抗原的抗体引起的免疫复合物性肾小管间质性肾炎在人类中很少见。我们的患者在移植后出现了终末期肾病和早期复发。IgG和C3沉积在近端肾小管的管状基底膜中很明显,这与电子显微镜观察到的沉积物相对应。在肾小球中发现了罕见的上皮下沉积物。该患者没有系统性红斑狼疮的证据,补体水平正常。与20份对照血清样本的阴性结果相比,该患者的血清样本与正常人肾脏的刷状缘发生反应。对刷状缘靶抗原的初步鉴定排除了巨膜蛋白、CD10和麦芽糖酶。我们推测,针对刷状缘抗原的抗体可导致直接的上皮损伤,积聚在管状基底膜中,并引发间质炎症反应。