Naidoo Sharan, Bütow Kurt W
Department of Maxillofacial and Oral Surgery, Facial Cleft Deformity Clinic, University of Pretoria, Pretoria, South Africa.
Department of Maxillofacial and Oral Surgery, Facial Cleft Deformity Clinic, University of Pretoria, Pretoria, South Africa ; Department of Health Sciences, University of KwaZulu-Natal, Durban ; Life Wilgers Hospital, Pretoria, South Africa.
Ann Maxillofac Surg. 2015 Jan-Jun;5(1):100-3. doi: 10.4103/2231-0746.161102.
To discuss the embryological basis, sequela and management of intraoral synechia, and to report on the incidence of this condition at a facial cleft deformity clinic (FCDC), with specific attention to two rare cases of mucosal bands involving the floor of the mouth and palate. Review of the literature and a retrospective analysis of FCDC and case report of two cases. During the period of 30 years (1983-2013), the FCDC - University of Pretoria has managed in excess of 4000 cases. A review of the clinic statistics revealed only six cases in which intraoral synechiae occurred. The rarity of this condition at the FCDC is in keeping with the rare incidence in the international literature. Four syndromic cases were identified. Three cases were cleft palate lateral synechia syndrome, and one was an orofacial digital syndrome. Two nonsyndromic cases were identified, and both cases involved the floor of the mouth and palate. The attending physicians and surgeons should be aware of the most appropriate timing for management of this condition, in order to avoid unwanted sequelae. Supportive care should be provided, and emergency airway protocol should be available for all cases. A differential diagnosis should be considered which includes syndromic conditions.
探讨口腔粘连的胚胎学基础、后遗症及处理方法,并报告面部裂畸形诊所(FCDC)中这种情况的发生率,特别关注两例罕见的涉及口腔底部和腭部的黏膜带病例。进行文献综述以及对FCDC病例进行回顾性分析并报告两例病例。在30年期间(1983 - 2013年),比勒陀利亚大学FCDC处理了超过4000例病例。对诊所统计数据的回顾显示,仅6例发生了口腔粘连。这种情况在FCDC的罕见性与国际文献中的低发生率相符。确定了4例综合征病例。3例为腭裂侧粘连综合征,1例为口面指综合征。确定了2例非综合征病例,均涉及口腔底部和腭部。主治医生和外科医生应了解处理这种情况的最合适时机,以避免不必要的后遗症。应提供支持性护理,并且应为所有病例制定紧急气道预案。应考虑鉴别诊断,包括综合征情况。