腘窝翼状胬肉综合征

Popliteal pterygium syndrome.

作者信息

Steinberg B, Saunders V

出版信息

Oral Surg Oral Med Oral Pathol. 1987 Jan;63(1):17-20. doi: 10.1016/0030-4220(87)90333-1.

Abstract

Popliteal pterygium syndrome (PPS) is a rare congenital disorder consisting of limb, genital, and orofacial malformations. Approximately fifty cases have been described, and the extremely variable nature of this syndrome has been shown. Two new cases of PPS are reported in this article. Surgical management and airway control are also described.

摘要

腘窝翼状胬肉综合征（PPS）是一种罕见的先天性疾病，包括肢体、生殖器和口面部畸形。大约已报道了50例病例，且该综合征具有极大的变异性。本文报道了2例PPS新病例。还描述了手术治疗和气道管理。