Yoon Byung-Nam, Kim Soo-Jung, Lim Mi-Jin, Han Jee-Young, Lee Kwang-Woo, Sung Jung-Joon, Ha Choong Kun, Choi Seong Hye
Department of Neurology, Inha University Hospital, Incheon 22332, Korea.
Division of Rheumatology, Department of Internal Medicine, Inha University Hospital, Incheon 22332, Korea.
Exp Neurobiol. 2015 Sep;24(3):252-5. doi: 10.5607/en.2015.24.3.252. Epub 2015 Sep 22.
A 25-year-old man presented with blurred vision and chronic headache. His brain MRI revealed bilateral frontal pachymeningeal enhancement with leptomeningeal enhancement. The patient had experienced recurrent oral ulcer and had anterior uveitis and papulopustules skin lesion. We diagnosed him with hypertrophic pachymeningitis (HP) associated with neuro-Behçet's disease (NBD). There have been few reports describing HP in patients with NBD. We report a case of NBD presenting as HP.
一名25岁男性出现视力模糊和慢性头痛。他的脑部磁共振成像(MRI)显示双侧额叶硬脑膜增厚强化伴软脑膜强化。该患者曾反复出现口腔溃疡,并有前葡萄膜炎和丘疹脓疱性皮肤病变。我们诊断他为与神经白塞病(NBD)相关的肥厚性硬脑膜炎(HP)。很少有报道描述NBD患者中的HP情况。我们报告一例以HP形式出现的NBD病例。