Bansal Sumit, Mahapatra Ashok Kumar
Department of Neurosurgery, All India Institute of Medical Sciences, Bhubaneswar, Odisha, India.
Asian J Neurosurg. 2015 Oct-Dec;10(4):350-2. doi: 10.4103/1793-5482.162730.
Terminal myelocystocele (TMC) is a rare form of spinal dysraphism. They constitute approximately 5% of skin covered lumbosacral masses. The TMC is composed of a low-lying conus medullaris with cystic dilatation of caudal central canal and a surrounding meningocele that extends from the conus to the skin. A 2-year-old female child presented with a large lumbosacral mass and weakness of both lower limbs since birth. Magnetic resonance imaging revealed a giant TMC. The child was operated on successfully. This is an interesting and rare case of "giant" TMC with partial sacral agenesis.
终末脊髓脊膜膨出(TMC)是一种罕见的脊柱裂畸形。它们约占腰骶部有皮肤覆盖肿物的5%。TMC由低位脊髓圆锥、尾侧中央管的囊性扩张以及从圆锥延伸至皮肤的周围脊膜膨出组成。一名2岁女童自出生以来腰骶部有一巨大肿物且双下肢无力。磁共振成像显示为巨大TMC。该患儿手术成功。这是一例伴有部分骶骨发育不全的“巨大”TMC的有趣且罕见病例。