Robinson Dominic, Rogers Barbara, Kapoor Ritu, Swan Joseph, Speas Gaylynn, Gutmann Rebecca
The Ohio State University Wexner Medical Center, Columbus, OH, USA.
J Investig Med High Impact Case Rep. 2014 Oct 10;2(4):2324709614553669. doi: 10.1177/2324709614553669. eCollection 2014 Oct-Dec.
Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant genetic disorder involving the abnormal communication of vascular structures. HHT typically presents with recurrent epistaxis and telangiectasis of the nasal and buccal mucosa, tongue, and lips. More serious manifestations of this disease include cerebral, pulmonary, gastrointestinal, and hepatic arteriovenous malformations. This case report details a 55-year-old male with HHT undergoing a five-box maze procedure for curative treatment of atrial fibrillation. Particular anesthetic considerations are described to reduce morbidity and mortality in this patient population.
遗传性出血性毛细血管扩张症（HHT）是一种常染色体显性遗传病，涉及血管结构的异常连通。HHT通常表现为反复鼻出血以及鼻和颊黏膜、舌头及嘴唇的毛细血管扩张。该病更严重的表现包括脑、肺、胃肠道和肝动静脉畸形。本病例报告详细介绍了一名患有HHT的55岁男性接受五盒迷宫手术以根治心房颤动的情况。文中描述了特殊的麻醉注意事项，以降低该患者群体的发病率和死亡率。
