Ross G J, Violi L, Friedman A C, Edmonds P R, Unger E
Department of Diagnostic Imaging, Temple University Hospital, Philadelphia, PA 19140.
J Comput Assist Tomogr. 1989 Mar-Apr;13(2):240-3. doi: 10.1097/00004728-198903000-00009.
Intravascular bronchioloalveolar tumor of the lung is an unusual neoplasm that usually presents as multiple pulmonary nodules in asymptomatic young women. The course of the disease is often indolent with some patients eventually dying of respiratory failure secondary to progressive tumor infiltration of the pulmonary interstitium. The cell of origin appears to be an endothelial cell, and epithelioid hemangioendothelioma of liver or other soft tissues is a pathologically identical neoplasm. Open lung biopsy is necessary for diagnosis. The radiologist should be aware of this tumor and suggest the diagnosis in the appropriate clinical setting.
肺血管内支气管肺泡瘤是一种罕见的肿瘤，通常表现为无症状年轻女性的多发性肺结节。疾病进程往往较为隐匿，一些患者最终死于呼吸衰竭，这是由于肿瘤逐渐浸润肺间质所致。肿瘤的起源细胞似乎是内皮细胞，肝脏或其他软组织的上皮样血管内皮瘤在病理上是与之相同的肿瘤。诊断需要进行开胸肺活检。放射科医生应了解这种肿瘤，并在适当的临床情况下提出诊断建议。
