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单卵双胞胎中伴有白血病前期综合征和Ph1染色体的骨髓单核细胞白血病

Myelomonocytic leukaemia with a preleukaemic syndrome and Ph1 chromosome in monozygotic twins.

作者信息

Svarch E, de la Torre E

出版信息

Arch Dis Child. 1977 Jan;52(1):72-4. doi: 10.1136/adc.52.1.72.

Abstract

A case of monozygotic twins with a preleukaemic phase of 3 1/2 years is reported. The final haematological picture was that of myelomonocytic leukaemia. The karyotype investigated in one twin during the final period of the disease showed a Ph1 chromosome.

摘要

报告了一例单卵双胞胎病例,其白血病前期长达3年半。最终血液学表现为骨髓单核细胞白血病。在疾病末期对其中一名双胞胎进行的核型分析显示有一条Ph1染色体。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d689/1546222/a2cefde249df/archdisch00821-0078-a.jpg

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本文引用的文献

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Myelomonocytic leukemia: disorderly proliferation of all marrow cells.髓单核细胞白血病:所有骨髓细胞的无序增殖。
Cancer. 1971 May;27(5):1221-30. doi: 10.1002/1097-0142(197105)27:5<1221::aid-cncr2820270530>3.0.co;2-p.
4
Epidemiology of acute myelomonocytic leukemia in children.
Cancer. 1973 Mar;31(3):516-9. doi: 10.1002/1097-0142(197303)31:3<516::aid-cncr2820310305>3.0.co;2-p.
5
Specificity of the Ph1 chromosome.Ph1染色体的特异性
Lancet. 1967 Dec 16;2(7529):1312-3. doi: 10.1016/s0140-6736(67)90429-1.
6
Letter: Philadelphia-chromosome-positive preleukaemic state.
Lancet. 1973 Nov 10;2(7837):1094. doi: 10.1016/s0140-6736(73)92711-6.
7
Philadelphia-chromosome-positive preleukaemic state.费城染色体阳性白血病前期状态
Lancet. 1972 Dec 9;2(7789):1227-8. doi: 10.1016/s0140-6736(72)92274-x.

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