Foster Jennifer H, Vasudevan Sanjeev A, John Hicks M, Schady Deborah, Chintagumpala Murali
1 Baylor College of Medicine, Pediatrics, 6701 Fannin Street, Houston, TX 77030, USA.
2 Baylor College of Medicine, Surgery, 6701 Fannin Street, Houston, TX 77030, USA.
Pediatr Dev Pathol. 2016 May-Jun;19(3):244-8. doi: 10.2350/15-05-1644-CR.1. Epub 2015 Oct 30.
Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare mesenchymal tumor of early childhood characterized by aggressive local infiltration of surrounding structures, rare metastases, and poor response to chemotherapy. Surgery alone appears to be the most effective treatment given the lack of predilection for metastasis and poor response to traditional chemotherapy. Below we report a patient with PMMTI successfully managed with surgery and observation and summarize the existing literature on histopathologic features and treatment of this lesion.
婴儿原始黏液样间叶肿瘤（PMMTI）是一种罕见的幼儿间叶肿瘤，其特征为对周围结构进行侵袭性局部浸润、转移罕见且对化疗反应不佳。鉴于其无转移倾向且对传统化疗反应不佳，单纯手术似乎是最有效的治疗方法。以下我们报告一例通过手术和观察成功治疗的PMMTI患者，并总结关于该病变组织病理学特征和治疗的现有文献。
