伴有布加综合征的下腔静脉原发性平滑肌肉瘤

Primary leiomyosarcoma of the inferior vena cava with Budd-Chiari syndrome.

作者信息

Imakita M, Yutani C, Ishibashi-Ueda H, Hiraoka H, Naito H

机构信息

Division of Pathology, National Cardiovascular Center, Osaka, Japan.

出版信息

Acta Pathol Jpn. 1989 Jan;39(1):73-7. doi: 10.1111/j.1440-1827.1989.tb02405.x.

DOI:10.1111/j.1440-1827.1989.tb02405.x

PMID:2652979

Abstract

A 44-year-old Japanese woman with leiomyosarcoma of the inferior vena cava is reported. She presented with Budd-Chiari syndrome and died of hepatic failure about 3 months after the onset of symptoms. The tumor arose from the middle segment of the inferior vena cava, occluded the inferior vena cava and projected into the right atrium. A total of 28 cases of Budd-Chiari syndrome due to primary leiomyosarcoma of the inferior vena cava are reviewed.

摘要

本文报道了一名44岁患有下腔静脉平滑肌肉瘤的日本女性。她表现为布加综合征，并在症状出现后约3个月死于肝衰竭。肿瘤起源于下腔静脉中段，阻塞了下腔静脉并突入右心房。本文回顾了总共28例由下腔静脉原发性平滑肌肉瘤引起的布加综合征病例。