Öztürk Mehmet, Siğirci Ahmet, Karadağ Neşe
Diyarbakır Children's Hospital, 21100 Diyarbakır, Turkey.
Faculty of Medicine, Inonu University, Elazig road, 15 km, Malatya, Turkey.
Springerplus. 2015 Nov 25;4:729. doi: 10.1186/s40064-015-1526-1. eCollection 2015.
Atypical teratoid rhabdoid tumour (ATRT) is a rare malignant tumour of the central nervous system with embryonal roots. The majority are seen in early childhood and location is often in the posterior fossa. Surgery, radiotherapy and chemotherapy are used in treatment. Knowledge of the localisation of the mass preoperatively is necessary for direction of the chemoradiotherapy and sufficient resection in surgery. Differentiation from other brain tumours is important because of poor prognosis and differences in treatment. In this paper it was aimed to present the clinical and radiological findings of an ATRT located in the cerebellopontine angle, which occurred with facial paralysis.
非典型畸胎样横纹肌样瘤（ATRT）是一种罕见的具有胚胎学根源的中枢神经系统恶性肿瘤。大多数病例见于儿童早期，且肿瘤常位于后颅窝。治疗方法包括手术、放疗和化疗。术前了解肿块的定位对于放化疗的指导以及手术中的充分切除至关重要。由于预后较差且治疗方法存在差异，与其他脑肿瘤进行鉴别诊断很重要。本文旨在介绍一例位于桥小脑角并伴有面瘫的ATRT的临床和影像学表现。
