Cuch Barbara, Nachulewicz Pawel, Wieczorek Andrzej Pawel, Wozniak Magdalena, Pac-Kozuchowska Elzbieta
From the Department of Paediatric Surgery and Traumatology (BC, PN), Department of Paediatric Radiology (APW, MW), and Department of Paediatric, Medical University of Lublin, Lublin, Poland (EP-K).
Medicine (Baltimore). 2015 Dec;94(49):e2270. doi: 10.1097/MD.0000000000002270.
Esophageal duplication cysts (EDCs) are rare developmental anomalies. They may occur anywhere along the esophagus with the predominant location in the thoracic segment. Presently, most are diagnosed prenatally or in early childhood. The prevalence of EDCs is estimated at 1 in 8200 live births. Usually, cysts are asymptomatic in the neonatal period, but they may cause respiratory distress or feeding difficulties depending on the size and location of the lesion.This report presents a female neonate with a cyst located in the right pleural cavity recognized prenatally. Computed tomography confirmed the diagnosis and revealed a round cystic mass in proximity to the left lung base. Thoracoscopic cyst excision was undertaken on day 15 after delivery. The postoperative period was uneventful. Histological cyst examination confirmed the diagnosis of foregut duplication.This case underlines the importance of early diagnosis and treatment of EDC, before symptoms and complications arise, and confirms that surgery in the neonatal period is safe and effective.
食管重复囊肿(EDC)是一种罕见的发育异常。它们可发生于食管的任何部位,主要位于胸段。目前,大多数在产前或幼儿期被诊断出来。据估计,EDC在活产婴儿中的患病率为8200分之一。通常,囊肿在新生儿期无症状,但根据病变的大小和位置,可能会导致呼吸窘迫或喂养困难。本报告介绍了一名产前被诊断出右胸腔有囊肿的女新生儿。计算机断层扫描证实了诊断,并显示左肺底部附近有一个圆形囊性肿块。出生后第15天进行了胸腔镜囊肿切除术。术后过程顺利。囊肿组织学检查确诊为前肠重复。该病例强调了在症状和并发症出现之前早期诊断和治疗EDC的重要性,并证实新生儿期手术是安全有效的。