周围性面神经麻痹，为颅底原始神经外胚层肿瘤的唯一表现。
Peripheral facial palsy, the only presentation of a primitive neuroectodermal tumor of the skull base.
作者信息
Kim Hyung Jin, Kang Ben, Joo Eun Young, Kim Eun Young, Kwon Young Se
机构信息
Department of Pediatrics, College of Medicine, Inha University, Incheon, Republic of Korea.
Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Republic of Korea.
出版信息
Int J Surg Case Rep. 2016;19:47-50. doi: 10.1016/j.ijscr.2015.12.019. Epub 2015 Dec 17.
INTRODUCTION
Peripheral facial palsy is rarely caused by primary neoplasms, which are mostly constituted of tumors of the central nervous system, head and neck, and leukemia.
PRESENTATION OF CASE
A 2-month-old male infant presented with asymmetric facial expression for 3 weeks. Physical examination revealed suspicious findings of right peripheral facial palsy. Computed tomography of the temporal bone revealed a suspicious bone tumor centered in the right petrous bone involving surrounding bones with extension into the middle ear cavity and inner ear. Subtotal resection of the tumor was performed due to crucial structures adjacent the mass. Histopathology and immunohistochemistry of the resected tumor was consistent with primitive neuroectodermal tumor.
CONCLUSION
We report a rare case of a primitive neuroectodermal tumor located at the skull base presenting with only peripheral facial palsy.
引言
周围性面瘫很少由原发性肿瘤引起，原发性肿瘤大多由中枢神经系统、头颈部肿瘤和白血病构成。
病例介绍
一名2个月大的男婴出现面部表情不对称3周。体格检查发现右侧周围性面瘫的可疑体征。颞骨计算机断层扫描显示右岩骨有一个可疑骨肿瘤，累及周围骨质并延伸至中耳腔和内耳。由于肿块邻近重要结构，故行肿瘤次全切除术。切除肿瘤的组织病理学和免疫组织化学检查结果与原始神经外胚层肿瘤一致。
结论
我们报告了一例罕见的位于颅底的原始神经外胚层肿瘤，仅表现为周围性面瘫。
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